index - Thérapie génique pour la DMD & physiopathologie du muscle squelettique Accéder directement au contenu

Dernières publications

Chiffres clés

48 Publications avec texte intégral

Open Access

67 %

Mots clés

Knockout Hear Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS CD38 Autophagy Morphogenesis DHPR α1S Muscle development Muscle Biology Becker BMD muscular dystrophy Cardiomyopathie Inbred C57BL Metabolism Becker muscular dystrophy BMD Male Dystrophin Inbred mdx Mice Energy Metabolism/drug effects DMD Mitochondrial fission Gene expression Muscle Strength Duchenne DMD dystrophy Cell Line Dystrophin central domain Cell Biology Centronuclear myopathy Dystrophin-EGFP Dynamin 2 Dystrophie Musculaire de Duchenne DMD DMO Cells Myogenesis Exon skipping Homeostasis L-Type Animals Ex-vivo Drp1 Skeletal muscle Calcium Cachexia Muscular dystrophy Cardiomyopathy Animal/physiopathology Antisense oligonucleotides Multi exon skipping Molecular docking Duchenne muscular dystrophy DMD Dystrophie musculaire de Becker Long noncoding RNA Liver Genomic Diseases CaVβs Duchenne muscular dystrophy Mdx mouse BMD Gene modifiers Muscle Gene Expression Regulation/drug effects CTNNB1 CaV subunits LncARN Multiresolution modeling Cultured Myotendinous junction Clinical trials Human Umbilical Vein Endothelial Cells MiARN Multi resolution modeling Allele‐specific silencing therapy Epigenetics Long QT Génomique Muscular Atrophy Muscular Dystrophy Immunoglobulin Fc Fragments/pharmacology Inhibitors Activin Receptors MES Delivery Becker muscular dystrophy Dystrophine Base Sequence Cell homeostasis Muscles/physiopathology Dystrophy Calcium Channels LncRNA NNOS Humans Invivo NAD+ Dystrophie Musculaire de Becker BMD Modificateurs de gènes Molecular Sequence Data Hepatocellular carcinoma LKB1